Consider IVIG when there is no response or a contraindication to corticosteroids, immunosuppressive agents or biologics (e.g. rituximab) in conjunction with one of the above.
First line therapy: cortiscosteroids
Second line: immunosuppressive agents
Third line: IVIG
Total dose 2 g/kg divided over 2 to 5 days every 4 weeks.
Dose every 6 weeks after 6 months of therapy.