IVIG is recommended for symptoms of grade 3 severity (able to walk with aid) or greater; or symptoms less than grade 3 severity that are progressing.
Treatment should be given within 2 weeks of symptom onset.
Re-treatment for patients who do not respond may be considered.
Adult: Total dose of 2 g/kg divided over 2 to 5 days.
Pediatric: Total dose of 2 g/kg divided over 2 days.
Repeat treatment with IVIG at 2 g/kg divided over 2 to 5 days.